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CG34

Recombinant Human GCDH/Glutaryl-CoA dehydrogenase, mitochondrial

10ug

840

756

现货

国产

CG34

Recombinant Human GCDH/Glutaryl-CoA dehydrogenase, mitochondrial

50ug

2520

2268

现货

国产

CG34

Recombinant Human GCDH/Glutaryl-CoA dehydrogenase, mitochondrial

500ug

12320

11088

现货

国产

CG34

Recombinant Human GCDH/Glutaryl-CoA dehydrogenase, mitochondrial

1mg

17600

15840

现货

国产

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  • Catalog# CG34
    Source E.coli
    Description Recombinant Human Glutaryl-CoA Dehydrogenase Mitochondrial/GCDH is produced with our E. coli expression system. The target protein is expressed with sequence (Arg45-Lys438) of Human GCDH fused with a His tag at the N-terminus.
    Names Glutaryl-CoA Dehydrogenase Mitochondrial, GCD, GCDH
    Accession # Q92947
    Formulation Supplied as a 0.2 μm filtered solution of 20mM HEPES, 150mM NaCl, pH 7.4
    Shipping The product is shipped on dry ice/ice packs.
    Storage Store at < -20°C, stable for 6 months after receipt.
    Please minimize freeze-thaw cycles.
    Purity Greater than 95% as determined by SEC-HPLC and reducing SDS-PAGE.
    Endotoxin Less than 0.1 ng/µg (1 IEU/µg).
    Amino Acid Sequence
    MNHKVHHHHHHMRPEFDWQDPLVLEEQLTTDEILIRDTFRTYCQERLMPRILLANRNEVFHREII SEMGELGVLGPTIKGYGCAGVSSVAYGLLARELERVDSGYRSAMSVQSSLVMHPIYAYGSEEQRQ KYLPQLAKGELLGCFGLTEPNSGSDPSSMETRAHYNSSNKSYTLNGTKTWITNSPMADLFVVWAR CEDGCIRGFLLEKGMRGLSAPRIQGKFSLRASATGMIIMDGVEVPEENVLPGASSLGGPFGCLNN ARYGIAWGVLGASEFCLHTARQYALDRMQFGVPLARNQLIQKKLADMLTEITLGLHACLQLGRLK DQDKAAPEMVSLLKRNNCGKALDIARQARDMLGGNGISDEYHVIRHAMNLEAVNTYEGTHDIHAL ILGRAITGIQAFTASK
    Background Glutaryl-CoA Dehydrogenase Mitochondrial (GCDH) is an enzyme that acts upon glutaryl-coenzyme A, creating crotonyl-coenzyme A. It plays a role in the metabolism of lysine, hydroxylysine and tryptophan. It uses electron transfer flavoprotein as its electron acceptor. Isoform Short is inactive Glutaryl-CoA and electron-transfer flavoprotein to (E)-but-2-enoyl-CoA, CO2 and reduced electron-transfer flavoprotein. A defect in this enzyme is associated with neurological condition glutaric acidemia type 1 and cause a progressive form of early-onset generalized dystonia.