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C992
Recombinant Human ETHE1/Ethylmalonic encephalopathy protein 1
10ug
1200
1080
现货
国产
-
C992
Recombinant Human ETHE1/Ethylmalonic encephalopathy protein 1
50ug
3520
3168
现货
国产
-
C992
Recombinant Human ETHE1/Ethylmalonic encephalopathy protein 1
500ug
12320
11088
现货
国产
-
C992
Recombinant Human ETHE1/Ethylmalonic encephalopathy protein 1
1mg
17600
15840
现货
国产
-
C992
Recombinant Human HSCO/Hepatoma subtracted clone one protein
10ug
1200
1080
现货
国产
-
C992
Recombinant Human HSCO/Hepatoma subtracted clone one protein
50ug
3520
3168
现货
国产
-
C992
Recombinant Human HSCO/Hepatoma subtracted clone one protein
500ug
12320
11088
现货
国产
-
C992
Recombinant Human HSCO/Hepatoma subtracted clone one protein
1mg
17600
15840
现货
国产
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Catalog# C992 Source HEK293 Description Recombinant Human Ethylmalonic Encephalopathy Protein 1/ETHE1 is produced by our mammalian expression system in human cells. The target protein is expressed with sequence (Leu13-Ala254) of Human ETHE1 fused with a 6His tag at the C-terminus. Names Protein ETHE1 Mitochondrial, Ethylmalonic Encephalopathy Protein 1, Hepatoma Subtracted Clone One Protein, ETHE1, HSCO Accession # O95571 Shipping The product is shipped at ambient temperature. Storage Store at < -20°C, stable for 6 months after receipt.
Please minimize freeze-thaw cycles.Purity Greater than 95% as determined by reducing SDS-PAGE. Endotoxin Less than 0.1 ng/μg (1 IEU/μg). Amino Acid Sequence LSQRGGSGAPILLRQMFEPVSCTFTYLLGDRESREAVLIDPVLETAPRDAQLIKELGLRLLYAVN THCHADHITGSGLLRSLLPGCQSVISRLSGAQADLHIEDGDSIRFGRFALETRASPGHTPGCVTF VLNDHSMAFTGDALLIRGCGRTDFQQGCAKTLYHSVHEKIFTLPGDCLIYPAHDYHGFTVSTVEE ERTLNPRLTLSCEEFVKIMGNLNLPKPQQIDFAVPANMRCGVQTPTAVDHHHHHHBackground Ethylmalonic Encephalopathy Protein 1 (ETHE1) belongs to the metallo-beta-lactamase superfamily. ETHE1 is widely expressed and localizes within the mitochondrial matrix. ETHE1 plays an important role in metabolic homeostasis in mitochondria. ETHE1 suppresses p53-induced apoptosis by preventing nuclear localization of RELA. Defects in ETHE1 are a cause of ethylmalonic encephalopathy, which is an autosomal recessive disorder that can lead to death in the first decade of life. It is also associated with persistent lactic acidemia and ethylmalonic and methylsuccinic aciduria.